Multiple unilateral maxillary dentigerous cysts in a non-syndromic patient: A case report and review of the literature

Summary 

Dentigerous cysts are the most common developmental odontogenic cysts of the jaw, arising from impacted, embedded or unerupted teeth. Although mostly solitary, multiple cysts occur in association with syndromes such as mucopolysaccharidosis type VI, cleidocranial dysplasia, basal cell nevus syndrome, and Gardner's syndrome. Multiple cysts in non-syndromic patients are extremely rare, occurring almost exclusively in the mandible. We report the case of a four-year-old girl with painless right-sided facial swelling, diagnosed with two dentigerous cysts in the right maxillary sinus, who successfully underwent enucleation. To our knowledge this is the only case of multiple unilateral maxillary dentigerous cysts in a healthy, non-syndromic patient.

Keywords: Dentigerous cyst, Odontogenic cyst, Odontogenic tumor, Odontoma, Facial swelling