International Journal of Pediatric Otorhinolaryngology Extra
Volume 1, Issue 2 , Pages 138-141, June 2006

Dizziness as presenting symptom of monostotic fibrous dysplasia

  • Domenico Leonardo Grasso

      Affiliations

    • Ear, Nose and Throat Department, IRCCS Burlo Garofolo, Trieste, Italy
    • Corresponding Author InformationCorresponding author at: ENT Department, Via dell’Istria, 65/1, 34137 Trieste, Italy. Tel.: +39 0403785256; fax: +39 0403785537.
  • ,
  • Veronica Ileana Guerci

      Affiliations

    • Genetic Department, IRCCS Burlo Garofolo, Trieste, Italy
  • ,
  • Paolo Di Emidio

      Affiliations

    • Maxillo Facial Department – IRCCS Burlo Garofolo, Trieste, Italy
  • ,
  • Raffaella De Vescovi

      Affiliations

    • Neurologic Department, IRCCS Burlo Garofolo, Trieste, Italy
  • ,
  • Maja Ukmar

      Affiliations

    • Radiology Department, Cattinara Hospital, Trieste, Italy
  • ,
  • Elisabetta Cattaruzzi

      Affiliations

    • Radiology Department, IRCCS Burlo Garofolo, Trieste, Italy
  • ,
  • Elisabetta Zocconi

      Affiliations

    • Ear, Nose and Throat Department, IRCCS Burlo Garofolo, Trieste, Italy

Received 5 September 2005; accepted 21 March 2006.

Summary 

Fibrous dysplasia is a rare, benign disease even though clinical picture may assume severe aspects. It presents a progressive replacement of normal bone structures by fibrous tissue which can involve one or more bone segments and, in some cases, it could be associated with skin lesions and endocrinopathies (McCune–Albright syndrome). It manifests clinically with dysmorphic syndrome, ophtalmologic or otologic signs. Vertigo in an uncommon presentation symptom. We report a case of monostotic fibrous dysplasia of the temporal bone presenting as dizziness in an 11-year-old boy and review the scientific literature.

Keywords: Fibrous dysplasia, Dizziness

 

PII: S1871-4048(06)00041-4

doi:10.1016/j.pedex.2006.03.003

International Journal of Pediatric Otorhinolaryngology Extra
Volume 1, Issue 2 , Pages 138-141, June 2006