International Journal of Pediatric Otorhinolaryngology Extra
Volume 1, Issue 2 , Pages 142-144 , June 2006

Enlarged vestibular aqueduct syndrome: A case of bilateral, sudden sensorineural hearing loss in a child

Received 1 February 2006 ,Revised 27 March 2006 ,Accepted 30 March 2006.

References 

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  9. Abe S, Shin-ichi U, Hoover D, Cohn E, Shinkawa H, Kimberling WJ. Fluctuating sensorineural hearing loss associated with enlarged vestibular aqueduct maps to 7q31, the region containing the pendred gene. Am. J. Med. Genet. 1999;82:322–328
  10. Jiann-Jou Y, Chin-Chu T, Hsiu-Mei H, Jiun-Yih S, Ching-Chyuan S, Shuan-Yow L. Hearing loss associated with enlarged vestibular aqueduct and mondini dysplasia caused by splice-site mutation in the pds gene. Hearing Res. 2005;199:22–30
  11. Pinto JA, Fernando CF, Marqui AC, Perfeito DJ, Ferreira RD, Silva RH. Enlarged vestibular aqueduct syndrome: report of 3 cases and literature review. Rev. Bras. Otorrinolaringol. 2005;71:386–391
  12. Kemperman MH, Stinckens C, Kumar S, Huygen PL, Joosten FM, Cremers CW. Progressive fluctuant hearing loss, enlarged vestibular aqueduct, and cochlear hypoplasia in branchio-oto-renal syndrome. Otol. Neurotol. 2001;22:637–643

☆ The views and opinions expressed in this manuscript do not necessarily reflect those of the United States Air Force, the Department of Defense, or the United States Government.

PII: S1871-4048(06)00042-6

doi: 10.1016/j.pedex.2006.03.004

International Journal of Pediatric Otorhinolaryngology Extra
Volume 1, Issue 2 , Pages 142-144 , June 2006

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