Bilateral nasal obstruction due to an intranasal craniopharyngioma

Received 21 August 2008; received in revised form 2 February 2009; accepted 7 February 2009. published online 19 March 2009.

Summary

A 14-year-old girl presented with a purely infrasellar adamantinomatous craniopharyngioma. Histologically benign, craniopharyngiomas occur predominantly extraaxially in the sellar and suprasellar regions; uniquely infrasellar craniopharyngiomas are extremely unusual. We discuss the embryology and treatment of this rare tumor.

Keywords: Craniopharyngioma, Intranasal, Infrasellar, Nasal obstruction, Rathke's pouch

a Division of Pediatric Otolaryngology, The Children's Hospital of Philadelphia, Philadelphia, PA, United States

b Department of Radiology, The Children's Hospital of Philadelphia, Philadelphia, PA, United States

c Department of Otorhinolaryngology/Head and Neck Surgery, University of Pennsylvania School of Medicine, Philadelphia, PA, United States

Corresponding author at: Division of Otolaryngology, 1st Floor, Wood Building, Children's Hospital of Philadelphia, Philadelphia, PA 19104, United States. Tel.: +1 215 590 3440; fax: +1 215 590 3986.

PII: S1871-4048(09)00015-X

doi:10.1016/j.pedex.2009.02.001

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