Atypical presentation of intracochlear schwannoma in a child

Abstract 

Intracochlear schwannoma (ICS) is a rare tumor that can cause significant hearing loss. Previous clinical reports on ICS have described this disease in adults. We present a pediatric patient with left-sided ICS who initially presented with a mild conductive hearing loss. We demonstrate the progression of the hearing loss over a span of several years through serial audiograms, as well as the process of diagnosis and treatment. This rare and unique case demonstrates that ICS can be found in young children.

Keywords: Intracochlear schwannoma (ICS), Conductive hearing loss (CHL), Word recognition score (WRS)