International Journal of Pediatric Otorhinolaryngology Extra RSS feed: Articles in Press. International Journal of Pediatric Otorhinolaryngology Extra is an online-only companion to the International Journal of Pediatric Otorhinolaryngology. International Journal of Pediatric Otorhinolaryngology Extra publishes case reports which have an important educational value but cannot be published in the printed journal due to lack of space. Case reports published in International Journal of Pediatric Otorhinolaryngology Extra are: •Peer reviewed to the usual high standards of IJPORL •Fully citable through digital object identifiers (DOI) •Rapidly available online via ScienceDirect, the world's leading online journal platform. Please note that as a new journal International Journal of Pediatric Otorhinolaryngology Extra is NOT currently covered by PubMed/MEDLINE® and does not have an impact factor. http://www.ijporlextra.com//inpress?rss=yesElsevier Inc.en © 2012 Published by Elsevier Inc. International Journal of Pediatric Otorhinolaryngology Extra1871-40482012-05-16 © 2012 Published by Elsevier Inc. healthpermissions@elsevier.comhttp://www.ijporlextra.com/article/PIIS187140481200024X/abstract?rss=yesAbstract: Purpose: A case presentation of a soft tissue lesion in an 8-month-old patient's left lateral tongue and review of the literature regarding infant tongue lesions. Methods: The patient's medical records were reviewed with summarization of care to date that care was received at presenting institution. A systematic literature review was then conducted using PedMed. Results: The differential diagnosis of infant tongue lesions is large, encompassing hemangiomas, lymphangiomas, thyroglossal duct cysts, teratomas, choristomas, infantile fibromatosis and rhabdomyosarcomas, among many others. Conclusion: Most infant tongue lesions are benign. However, given the aggressive propensity of infantile fibromatosis and rhabdomyosarcomas, all infant tongue lesions must be characterized.Infant tongue lesions: A case presentation and review of the literature - Corrected ProofJacob B. Hunter10.1016/j.pedex.2012.04.001International Journal of Pediatric Otorhinolaryngology Extra (2012)2012-05-16International Journal of Pediatric Otorhinolaryngology Extra2012-05-16CASE REPORThttp://www.ijporlextra.com/article/PIIS1871404812000251/abstract?rss=yesAbstract: Angiokeratomas are vascular malformations that usually appear as multiple or solitary cutaneous plaques with several clinical variants. Mucosal involvement, including the oral cavity, is occasionally found either as a component of the systemic variety, called angiokeratoma corporis diffusum, or associated with cutaneous lesions in more locations. Isolated oral involvement is rare. Isolated involvement of tongue with multiple angiokeratomas (without cutaneous or metabolic disease) and without plaque formation has been reported only thrice before this report. We here in report fourth case of this rare entity affecting a 16-year-old female. Beside this, our case is first such case in indexed literature with significant involvement of both dorsal and ventral surfaces of tongue.Isolated multiple angiokeratoma of tongue—A case report and review of literature - Corrected ProofSuhail Amin Patigaroo, Nazir A. Khan, Sheikh Manzoor, Nalini Gupta, Priti Jain, Mohammed Shakeel10.1016/j.pedex.2012.04.002International Journal of Pediatric Otorhinolaryngology Extra (2012)2012-05-14International Journal of Pediatric Otorhinolaryngology Extra2012-05-14CASE REPORThttp://www.ijporlextra.com/article/PIIS1871404812000238/abstract?rss=yesAbstract: Basal cell naevus syndrome is a rare hereditary autosomal dominant disease. We present the case of a three-year-old boy with the syndrome, associated with a nasal dermoid sinus cyst. Review of the literature revealed only one similar case of this syndrome with a nasal dermoid sinus cyst. PTCH1, the gene responsible for the disease in this case, is expressed in the neural tube of the developing embryo and mutations can lead to developmental anomalies. This fact combined with the knowledge that nasal dermoid sinus cysts are remains of an ectodermal extension of the dura, explains the association of Basal cell naevus syndrome with a nasal dermoid sinus cyst. We suggest that it should be adopted as a minor diagnostic criterion.Midline nasal dermoid sinus cyst in basal cell naevus syndrome (BCNS or Gorlin syndrome): A case report and review - Corrected ProofK. Pilaete, F. Roelens, K. Claes, J. Verfaillie10.1016/j.pedex.2012.03.004International Journal of Pediatric Otorhinolaryngology Extra (2012)2012-04-23International Journal of Pediatric Otorhinolaryngology Extra2012-04-23CASE REPORThttp://www.ijporlextra.com/article/PIIS1871404812000226/abstract?rss=yesAbstract: We report a rare neonatal case of retropharyngeal abscess (RPA). A 4-day-old neonate was seen for stridor without fever. CT and MRI examinations detected an RPA together with the air-bubble sign. Surgical drainage of the abscess yielded copious pus. He was treated with antibiotics after surgery and made an uneventful recovery. Respiratory symptoms develop more easily than fever in neonatal RPA. According to previous reports, air-bubble findings and a mass localized on the left side tend to be found during radiological examinations. These radiological features are common in neonates with pyriform sinus fistulae, which can cause RPA.Retropharyngeal abscess in a neonate: A case report and literature review - Corrected ProofYuji Kanazawa, Masatsugu Asai, Yuichi Adachi, Taketoshi Yoshida, Toshiko Itazawa, Ayako Shimao, Tomomi Inomata, Hideki Abe, Yukio Watanabe10.1016/j.pedex.2012.03.003International Journal of Pediatric Otorhinolaryngology Extra (2012)2012-04-19International Journal of Pediatric Otorhinolaryngology Extra2012-04-19CASE REPORThttp://www.ijporlextra.com/article/PIIS1871404812000214/abstract?rss=yesAbstract: Relapsing polychondritis (RP) is a rare multisystem disease of unknown etiology characterized by recurrent and progressive course of destructive and inflammatory lesions of cartilage. Its association with familial Mediterranean fever (FMF) has been reported in only two adult cases. We present here a 13-year old girl with FMF and selective immunoglobulin (Ig) A deficiency who developed RP. To our knowledge, this case is the first well documented child and the third patient in the literature with FMF and RP together with selective Ig A deficiency which has not been reported with both disorders before.Relapsing polychondritis in a child with familial Mediterranean fever and selective immunoglobulin a deficiency - Corrected ProofGülay Demircin, Erdoğan Okur, Hazfa Uçur, Meltem Uğraş, Tolga Şen10.1016/j.pedex.2012.03.002International Journal of Pediatric Otorhinolaryngology Extra (2012)2012-04-16International Journal of Pediatric Otorhinolaryngology Extra2012-04-16CASE REPORThttp://www.ijporlextra.com/article/PIIS1871404812000123/abstract?rss=yesAbstract: Synovial cell sarcoma is a rare subtype of soft tissue sarcoma. It usually affects the extremities and laryngeal tumours are extremely rare. We present the case of an 11 year old boy with synovial cell sarcoma arising from the right aryepiglottic fold which was not deemed resectable at the time of diagnosis. He underwent pre-operative chemoradiotherapay followed by total laryngectomy and remains disease free over 6 years after treatment. There were also multiple clinical, psychological and social challenges faced during the rehabilitation of this paediatric laryngectomy patient.Laryngeal synovial cell sarcoma in an 11 year old boy: Challenges of management and rehabilitation - Corrected ProofC. Simon, D.P. Crampsey, F.B. MacGregor10.1016/j.pedex.2012.02.002International Journal of Pediatric Otorhinolaryngology Extra (2012)2012-04-12International Journal of Pediatric Otorhinolaryngology Extra2012-04-12CASE REPORThttp://www.ijporlextra.com/article/PIIS1871404812000202/abstract?rss=yesAbstract: We present a case of a child with recurrent parotid abscess where a feather was found within the abscess cavity at the second incisional drainage procedure.‘Is it a bird? No it's a feather!’ Parotid abscesses and the perils of feather pillows - Corrected ProofGemma Pilgrim, Rebecca Heywood, Romana Kuchai10.1016/j.pedex.2012.03.001International Journal of Pediatric Otorhinolaryngology Extra (2012)2012-04-05International Journal of Pediatric Otorhinolaryngology Extra2012-04-05CASE REPORThttp://www.ijporlextra.com/article/PIIS1871404812000135/abstract?rss=yesAbstract: Lymphangioma has been known to develop in head and neck region. However, lymphangiomas origin from the auricular region is extremely rare, and has been reported only once in the English literature. Here, we introduce a case of large lymphangioma that originated from the posterior aspect of the auricle. An 18-month-old boy visited our hospital with a palpable mass growing on the posterior aspect of the auricle from the age of 6 months. Radiological studies showed a lobulated mass on the superoposterior aspect of the right ear, which was thought to be a hemangiolymphamgioma. As hemangiomas usually regress spontaneously, we observed this mass closely for about 1 year. There was no noticeable regression of the mass, which appeared multi-septated in imaging studies. We decided to excise the mass rather than perform sclerotherapy. The multilobulated mass, originating from the posterior aspect of the auricle extending to the anterior parotid area, was excised completely and was confirmed to be a lymphangioma pathologically. Here, we report this rare lymphangioma originating from the posterior aspect of the auricle with a literature review.A case of large auricular lymphangioma - Corrected ProofJee-nam Song, So-Lyung Jung, Sung-Hak Lee, Shi-Nae Park10.1016/j.pedex.2012.02.003International Journal of Pediatric Otorhinolaryngology Extra (2012)2012-03-16International Journal of Pediatric Otorhinolaryngology Extra2012-03-16CASE REPORThttp://www.ijporlextra.com/article/PIIS1871404812000147/abstract?rss=yesAbstract: Enterobious vermicularis is the most common nematode that infects humans. The location of infestation is often localized to the gastrointestinal or genitourinary tracts. It inhabits the intestinal lumen, but it was observed that ectopic infections were rarely documented. This study presents a rare case of E. vermicularis pin worm granuloma at the neck; this is the first reported case to the best of our knowledge from our search in the literature. The patient was a boy presented with a one-year history of multiple cervical lymphadenopathy with prominent unilateral submandibular swelling. Multiple investigations, including fine needle aspiration cytology (FNAC), serial full blood count and full blood picture, and computed tomography (CT) scan of the neck were done to rule out causes of swelling. However, our final diagnosis after excision of the prominent submandibular swelling came back as E. vermicularis granuloma of the neck.Enterobious vermicularis granuloma of the neck: An unusual neck mass - Corrected ProofM.S. Norasnieda, M. Irfan, A. Khairuddin, J. Zakaria10.1016/j.pedex.2012.02.004International Journal of Pediatric Otorhinolaryngology Extra (2012)2012-03-16International Journal of Pediatric Otorhinolaryngology Extra2012-03-16CASE REPORT